CAS NO: | 102636-82-8 |
包装: | 5mg |
Glutarylcarnitine丙二酸尿症和I型戊二酸尿症的重要诊断代谢物。
Cas No. | 102636-82-8 |
别名 | 戊二酰基肉碱 |
Canonical SMILES | C[N+](C)(C)C[C@H](OC(CCCC([O-])=O)=O)CC(O)=O |
分子式 | C12H21NO6 |
分子量 | 275.3 |
溶解度 | Soluble in DMSO |
储存条件 | Store at -20°C |
General tips | For obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while. |
Shipping Condition | Evaluation sample solution : ship with blue ice All other available size: ship with RT , or blue ice upon request |
产品描述 | Glutarylcarnitine is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes. Malonylcarnitine and Glutarylcarnitine are important diagnostic metabolites in the screening of dried blood spots by tandem mass spectrometry[1]. [1]. Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27(6):789-90. |