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2-Hydroxy-2-methylbutanoic acid
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
2-Hydroxy-2-methylbutanoic acid图片
CAS NO:3739-30-8
包装:1g
市场价:446元

产品介绍
2-Hydroxy-2-methylbutanoicacid是一种非正常的代谢物,和羟基戊二酸尿症以及枫糖尿病有关。
Cas No.3739-30-8
别名2-羟基-2-甲基丁酸
Canonical SMILESCCC(C)(O)C(O)=O
分子式C5H10O3
分子量118.13
溶解度Soluble in DMSO
储存条件Store at -20°C
General tipsFor obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while.
Shipping ConditionEvaluation sample solution : ship with blue ice
All other available size: ship with RT , or blue ice upon request
产品描述

2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.

[1]. Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May;(102):29-71; discussion 95-109.