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2-Methylsuccinic acid
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
2-Methylsuccinic acid图片
CAS NO:498-21-5
包装与价格:
包装价格(元)
500 mg电议
1 g电议
1 mL*10 mM(in DMSO)电议

产品名称
Pyrotartaric Acid
甲基丁二酸
Methylbutanedioic acid
产品介绍
2-Methylsuccinic acid 是乙基丙二酸脑病的主要生化指标,是人体液中的正常代谢物。

产品描述

Methylsuccinic acid is a normal metabolite found in human fluids. Increased urinary levels of Methylsuccinic acid (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea.

Cas No.

498-21-5

分子式

C5H8O4

分子量

132.115

别名

Pyrotartaric Acid;甲基丁二酸;Methylbutanedioic acid;2-Methylsuccinic acid

储存和溶解度

DMSO:200 mM
Powder: -20°C for 3 years
In solvent: -80°C for 2 years