L-Homocitrulline通过尿素循环途径获得的homoargininosuccinate代谢成高精氨酸(homoarginine)，L-Homocitrulline的代谢异常会导致赖氨酸尿蛋白不耐受(LPI)。
CAS：1190-49-4
分子式：C7H15N3O3
分子量：189.21
纯度：98%
存储：Store at -20°C

Background:

L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).

[1]. Kato T, et al. Homocitrullinuria and homoargininuria in lysinuric protein intolerance. J Inherit Metab Dis. 1989;12(2):157-61.