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2-Methylsuccinic acid
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
2-Methylsuccinic acid图片
CAS NO:498-21-5
包装:1g
规格:98%
市场价:445元
分子量:132.12

产品介绍
2-Methylsuccinicacid是人体液中的一种正常代谢物,是乙基丙二酸脑病的主要生化指标。
CAS:498-21-5
分子式:C5H8O4
分子量:132.12
纯度:98%
存储:Store at -20°C

Background:

2-Methylsuccinic acid is a normal metabolite in human fluids and the main biochemical measurable features in ethylmalonic encephalopathy.


2-Methylsuccinic acid is a normal metabolite in human fluids and the main biochemical measurable features in ethylmalonic encephalopathy[1]. The underlying biochemical defect involves isoleucine catabolism[2].



[1]. Grosso S, et al. Ethylmalonic encephalopathy: further clinical and neuroradiological characterization. J Neurol. 2002 Oct;249(10):1446-50. [2]. Nowaczyk MJ, et al. Ethylmalonic and methylsuccinic aciduria in ethylmalonic encephalopathy arise from abnormal isoleucine metabolism. Metabolism. 1998 Jul;47(7):836-9.