Twinkle蛋白(TWINL)抗体

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Twinkle蛋白(TWINL)抗体

本产品不向个人销售，仅用作科学研究，不用于任何人体实验及非科研性质的动物实验。

产品名称

共济失调蛋白8抗体
Anti-TWNK

产品介绍

靶标：

TWNK

产品别名：

ATXN8； C10orf2； IOSCA； MTDPS7； PEO； PEO1； PEOA3； PRLTS5； SANDO； SCA8； TWINL； TWNK； twinkle mtDNA helicase； twinkle mtDNA helicase； twinkle mtDNA helicase； T7 gp4-like protein with intramitochondrial nucleoid localization； T7 helicase-related protein with intramitochondrial nucleoid localization； T7-like mitochondrial DNA helicase； ataxin 8； progressive external ophthalmoplegia 1 protein； twinkle protein, mitochondrial； Twinkle蛋白(TWINL)；共济失调蛋白8；

背景信息：

This gene encodes a hexameric DNA helicase which unwinds short stretches of double-stranded DNA in the 5' to 3' direction and, along with mitochondrial single-stranded DNA binding protein and mtDNA polymerase gamma, is thought to play a key role in mtDNA replication. The protein localizes to the mitochondrial matrix and mitochondrial nucleoids. Mutations in this gene cause infantile onset spinocerebellar ataxia (IOSCA) and progressive external ophthalmoplegia (PEO) and are also associated with several mitochondrial depletion syndromes. Alternative splicing results in multiple transcript variants encoding distinct isoforms.

宿主：Rbt
类型：Pab
同种型:IgG
应用：WB
纯化方式：亲和纯化
偶联物：Unconjugated
性状：液体
存储溶液：参阅说明书
浓度：Batch dependent (Please refer to the vial label for the specific concentration.)
稀释比例: Optimal dilutions/concentrations should be determined by the end user
储存：经常使用则4°C保存。-20°C保存不超过两年。避免反复冻融。
注意事项：仅供实验室使用。不适用于人类或动物的任何临床，治疗或诊断用途。不适合动物或人类食用。