线粒体COQ2抗体

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线粒体COQ2抗体

本产品不向个人销售，仅用作科学研究，不用于任何人体实验及非科研性质的动物实验。

产品名称

Anti-COQ2
Anti-coenzyme Q2, polyprenyltransferase Antibody

产品介绍

靶标：

COQ2

产品别名：

CL640； COQ10D1； MSA1； PHB:PPT； COQ2； coenzyme Q2, polyprenyltransferase； coenzyme Q2, polyprenyltransferase； 4-hydroxybenzoate polyprenyltransferase, mitochondrial； 4-HB polyprenyltransferase； 4-hydroxybenzoate decaprenyltransferase； PHB:polyprenyltransferase； coenzyme Q2 4-hydroxybenzoate polyprenyltransferase； coenzyme Q2 homolog, prenyltransferase； para-hydroxybenzoate-polyprenyltransferase, mitochondrial；线粒体COQ2；

背景信息：

This gene encodes an enzyme that functions in the final steps in the biosynthesis of CoQ (ubiquinone), a redox carrier in the mitochondrial respiratory chain and a lipid-soluble antioxidant. This enzyme, which is part of the coenzyme Q10 pathway, catalyzes the prenylation of parahydroxybenzoate with an all-trans polyprenyl group. Mutations in this gene cause coenzyme Q10 deficiency, a mitochondrial encephalomyopathy, and also COQ2 nephropathy, an inherited form of mitochondriopathy with primary renal involvement. [provided by RefSeq, Oct 2009],

宿主：Rbt
类型：Pab
同种型:IgG
应用：WB
纯化方式：亲和纯化
偶联物：Unconjugated
性状：液体
存储溶液：参阅说明书
浓度：Batch dependent (Please refer to the vial label for the specific concentration.)
稀释比例: Optimal dilutions/concentrations should be determined by the end user
储存：经常使用则4°C保存。-20°C保存不超过两年。避免反复冻融。
注意事项：仅供实验室使用。不适用于人类或动物的任何临床，治疗或诊断用途。不适合动物或人类食用。