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重组α葡萄糖苷酶/溶酶体α-葡糖苷酶蛋白
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。

产品名称
重组酸性葡糖苷酶α(GaA)蛋白
Recombinant GAA
产品介绍
基因名:

GAA


产品别名:

LYAG; GAA; alpha glucosidase; alpha glucosidase; lysosomal alpha-glucosidase; acid maltase; aglucosidase alfa; glucosidase alpha, acid; α葡萄糖苷酶/溶酶体α-葡糖苷酶; 酸性葡糖苷酶α(GaA);


背景信息:
This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008].

标签:His-tag   
分类:Recombinant  
类型:Protein   
偶联物:Unconjugated
内毒素水平:按批次,参阅瓶身标签
性状:Liquid
浓度:Batch dependent (Please refer to the vial label for the specific concentration.)
纯化类型:purified
内含物:不含防腐剂
应用:Positive Control;Immunogen;SDS-PAGE;WB.
储存:2-8°C不超过一个月,-80°C不超过12个月。避免反复冻融。
注意事项:仅供实验室使用。不适用于人类或动物的任何临床,治疗或诊断用途。不适合动物或人类食用。