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重组γ-5羧酸合成酶蛋白
本产品不向个人销售，仅用作科学研究，不用于任何人体实验及非科研性质的动物实验。

产品名称
Recombinant ALDH18A1
Recombinant aldehyde dehydrogenase 18 family member A1 protein
产品介绍
基因名：

ALDH18A1


产品别名：

ADCL3； ARCL3A； GSAS； P5CS； PYCS； SPG9； SPG9A； SPG9B； ALDH18A1； aldehyde dehydrogenase 18 family member A1； aldehyde dehydrogenase 18 family member A1； delta-1-pyrroline-5-carboxylate synthase； Spastic paraplegia-9 (spastic paraparesis with amyotrophy, cataracts and gastroesophageal reflux)； aldehyde dehydrogenase family 18 member A1； delta-1-pyrroline-5-carboxylate synthetase； delta1-pyrroline-5-carboxlate synthetase； pyrroline-5-carboxylate synthetase (glutamate gamma-semialdehyde synthetase)； spastic paraplegia 9 (autosomal dominant)； γ-5羧酸合成酶；


背景信息：
This gene is a member of the aldehyde dehydrogenase family and encodes a bifunctional ATP- and NADPH-dependent mitochondrial enzyme with both gamma-glutamyl kinase and gamma-glutamyl phosphate reductase activities. The encoded protein catalyzes the reduction of glutamate to delta1-pyrroline-5-carboxylate, a critical step in the de novo biosynthesis of proline, ornithine and arginine. Mutations in this gene lead to hyperammonemia, hypoornithinemia, hypocitrullinemia, hypoargininemia and hypoprolinemia and may be associated with neurodegeneration, cataracts and connective tissue diseases. Alternatively spliced transcript variants, encoding different isoforms, have been described for this gene. [provided by RefSeq, Jul 2008]

标签：His-tag   
分类：Recombinant  
类型：Protein   
偶联物：Unconjugated
内毒素水平：按批次，参阅瓶身标签
性状:Liquid
浓度：Batch dependent (Please refer to the vial label for the specific concentration.)
纯化类型：purified
内含物：不含防腐剂
应用:Positive Control;Immunogen;SDS-PAGE;WB.
储存：2-8°C不超过一个月，-80°C不超过12个月。避免反复冻融。
注意事项：仅供实验室使用。不适用于人类或动物的任何临床，治疗或诊断用途。不适合动物或人类食用。